In this educational exhibit we propose to achieve these objectives: To recognize the imaging appearance of cavernous transformation of portal vein; – To. While, ascites is a common sign in patients with POEMS, it is unfrequently associated with portal cavernomatosis and portal hypertension. We report a case of a. Rev Esp Enferm Dig. Mar;(3) Portal hydatid with secondary cavernomatosis. Rodríguez Sanz MB(1), Roldán Cuena MD(2), Blanco Álvarez.

Author: Kegami Gardajora
Country: Mozambique
Language: English (Spanish)
Genre: Business
Published (Last): 7 September 2004
Pages: 443
PDF File Size: 2.5 Mb
ePub File Size: 9.3 Mb
ISBN: 574-3-32783-255-1
Downloads: 52585
Price: Free* [*Free Regsitration Required]
Uploader: Tegami

After the initial evaluation, the patient experienced progressive deterioration over the following 4 months.

SONOWORLD : Portal cavernoma (cavernous transformation of the portal vein)

Personal information Silvia Pellegrino, silviapellegrino82 libero. There was no history of drugs, tobacco or alcohol abuse. The association with Castleman disease is generally related to a worse prognosis.

Dimarco 1G. Case 3 Case 3. The free cavernoatosis and lambda light chains concentrations were About Blog Go ad-free.

[Portal hypertension due to cavernomatosis of the portal vein].

ECR Poster No.: These changes lead to a central liver hypertrophy and peripheral liver atrophy 8. The serum immunofixation test showed an IgA lambda biclonal band, while urine serum test was negative.

Treatment with diuretics was started. There was progression of ascites, lower limbs edemas and developed skin hyperpigmentation, with predominance on the face, extremities, and mucous membranes.


Whereas portal hypertension can in some cases be treated with TIPSthe absence of normal portal circulation usually makes this impossible.

On physical examination, moderate abdominal ascites and hepatosplenomegaly was present only. Case 10 Case In patients whose portal vein does not recanalize, or only partially re-canalizes, collateral veins thought to be paracholedochal veins dilate and become serpiginous.

[Portal hypertension due to cavernomatosis of the portal vein].

Sonography usually shows PVT as a hyperechoic lesion within the lumen of the portal vein. Extravascular volume overload is one of the most common manifestations of POEMS, characterized by peripheral edemas, pleural effusion, ascites, and pericardial effusion. Findings and procedure details MRI, CT and Doppler ultrasound can be useful in detecting these pathologies by identifying the most common signs. While, ascites is a common sign in patients with POEMS, it is unfrequently associated with portal cavernomatosis cavernomattosis portal hypertension.

Portal hydatid with secondary cavernomatosis.

What to look for? Castleman disease, osteosclerotic inju ries and the elevated vascular endothelial growth factor VEGF.

These vessels drain variably into the left and right portal veins or more distally into the liver. Additional communications cavernonatosis also be identified with the pericholecystic veins. Following thrombosis, the portal vein may or may not re-canalize. Re-canalisation is seen more frequently in patients without cirrhosis or disease of the liver leading to inherently increased resistance to portal flow.


Doppler examination can be carried out at the same time to evaluate for portal hypertension. Dimarco 1T.

Trujillo Calderon 2J. However, clots exhibit variable echogenicity and may, if portla formed, be hypoechoic or anechoic.

Cavernous transformation of the portal vein: In addition, there were no cases portal thrombosis or hepatic vein thrombosis according to Doppler evaluation. Picone 1S. Learning objectives In this educational exhibit we propose to achieve these objectives: Picone 1G. In conclusion, POEMS syndrome is an extremely rare disease and may include a wide variety of clinical manifestations.

Caudate Lobe Ipertrophy arrows. On the first click the button podtal be activated and you can then share the poster with a second click. Case 2 Case 2. Bartolotta 1S. Additionally, there are changes in liver shape which are somewhat different to cavdrnomatosis seen in cirrhosis 2.